- E75.4 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2024 edition of ICD-10-CM E75.4 became effective on October 1, 2022.
- This is the American ICD-10-CM version of E75.4 – other international versions of ICD-10 E75.4 may differ.
ICD-10-CM E75.4 is grouped within Diagnostic Related Group(s):
- 056 Degenerative nervous system disorders with mcc
- 057 Degenerative nervous system disorders without mcc
Applicable To
- Batten disease
- Bielschowsky-Jansky disease
- Kufs disease
- Spielmeyer-Vogt disease
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2016 (effective 10/1/2015): No change
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
- 2024 (effective 10/1/2022): No change
Diagnosis Index entries containing back-references to E75.4:
- retina > Batten disease (-Mayou) E75.4
- lipidosis > in G31.2
- cerebral > lipidosis E75.4
- Batten\’s or Batten-Mayou > retina, retinal H35.9
- amaurotic (Bielschowsky(-Jansky)) (family) (infantile (late)) (juvenile (late)) (Vogt-Spielmeyer) > Idiot, idiocy (congenital) F73
- cerebral (infantile) (juvenile) (late) > Lipidosis E75.6
- cerebroretinal > Lipidosis E75.6