Type 1 Excludes
- autosomal recessive agammaglobulinemia (Swiss type) (D80.0)
- Codes Description
- D81.0
Severe combined immunodeficiency [SCID] with reticular dysgenesis
- D81.1
Severe combined immunodeficiency [SCID] with low T- and B-cell numbers
- D81.2
Severe combined immunodeficiency [SCID] with low or normal B-cell numbers
- D81.3
Adenosine deaminase [ADA] deficiency
- D81.4
Nezelof’s syndrome
- D81.5
Purine nucleoside phosphorylase [PNP] deficiency
- D81.6
Major histocompatibility complex class I deficiency
- D81.7
Major histocompatibility complex class II deficiency
- D81.8
Other combined immunodeficiencies
- D81.9
Combined immunodeficiency, unspecified