| Type 1 Excludes |
| (Abt-) Letterer-Siwe disease (C96.0) |
| eosinophilic granuloma (C96.6) |
| Hand-Schüller-Christian disease (C96.5) |
| histiocytic sarcoma (C96.A) |
| histiocytosis X, multifocal (C96.5) |
| histiocytosis X, unifocal (C96.6) |
| malignant histiocytosis (C96.A) |
| Langerhans-cell histiocytosis, multifocal (C96.5) |
| Langerhans-cell histiocytosis NOS (C96.6) |
| Langerhans-cell histiocytosis, unifocal (C96.6) |
| leukemic reticuloendotheliosis or reticulosis (C91.4-) |
| lipomelanotic reticuloendotheliosis or reticulosis (I89.8) |
|
D76.1 |
|
Hemophagocytic lymphohistiocytosis |
|
D76.2 |
|
Hemophagocytic syndrome, infection-associated |
|
D76.3 |
|
Other histiocytosis syndromes |
