- M04.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2024 edition of ICD-10-CM M04.1 became effective on October 1, 2022.
- This is the American ICD-10-CM version of M04.1 – other international versions of ICD-10 M04.1 may differ.
ICD-10-CM M04.1 is grouped within Diagnostic Related Group(s):
- 545 Connective tissue disorders with mcc
- 546 Connective tissue disorders with cc
- 547 Connective tissue disorders without cc/mcc
Applicable To
- Familial Mediterranean fever
- Hyperimmunoglobin D syndrome
- Mevalonate kinase deficiency
- Tumor necrosis factor receptor associated periodic syndrome [TRAPS]
Code History
- 2017 (effective 10/1/2016): New code
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
- 2024 (effective 10/1/2022): No change
Diagnosis Index entries containing back-references to M04.1:
- Mediterranean fever, familial > in (due to) E22.0
- mevalonate kinase > Deficiency, deficient
- familial > Mediterranean A23.9
- periodic (Mediterranean) > Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) R50.9
- fever > Mediterranean
- familial > fever M04.1
- hyperimmunoglobulin D > Syndrome
- periodic fever > Syndrome
- tumor necrosis factor receptor associated periodic (TRAPS) > Syndrome