- I27.0 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
- The 2024 edition of ICD-10-CM I27.0 became effective on October 1, 2022.
- This is the American ICD-10-CM version of I27.0 – other international versions of ICD-10 I27.0 may differ.
ICD-10-CM I27.0 is grouped within Diagnostic Related Group(s):
- 314 Other circulatory system diagnoses with mcc
- 315 Other circulatory system diagnoses with cc
- 316 Other circulatory system diagnoses without cc/mcc
Applicable To
- Heritable pulmonary arterial hypertension
- Idiopathic pulmonary arterial hypertension
- Primary group 1 pulmonary hypertension
- Primary pulmonary arterial hypertension
Type 1 Excludes
- persistent pulmonary hypertension of newborn (P29.30)
- pulmonary hypertension NOS (I27.20)
- secondary pulmonary arterial hypertension (I27.21)
- secondary pulmonary hypertension (I27.29)
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
- 2016 (effective 10/1/2015): No change
- 2017 (effective 10/1/2016): No change
- 2018 (effective 10/1/2017): No change
- 2019 (effective 10/1/2018): No change
- 2020 (effective 10/1/2019): No change
- 2021 (effective 10/1/2020): No change
- 2022 (effective 10/1/2021): No change
- 2024 (effective 10/1/2022): No change
Diagnosis Index entries containing back-references to I27.0:
- pulmonary (idiopathic) > Arteriosclerosis, arteriosclerotic (diffuse) (obliterans) (of) (senile) (with calcification) I70.90
- Ayerza\’s (pulmonary artery sclerosis with pulmonary hypertension) > Disease, diseased
- black > heart (organic) I51.9
- primary (idiopathic) > hypertensive (vascular) I27.20
- lesser circulation > Hypertension, hypertensive (accelerated) (benign) (essential) (idiopathic) (malignant) (systemic) I10
- primary (idiopathic) > pulmonary I27.20
- pulmonary > Sclerosis, sclerotic
- artery > pulmonary I27.0
- Arrillaga-Ayerza > Syndrome
- Ayerza (-Arrillaga) > Syndrome
- cardiacos negros > Syndrome
- pulmonary > Syndrome
- arteriosclerosis > pulmonary I27.0