- E88.1 is a billable/specific ICD-10-CM code that can be used to indicate a diagnosis for reimbursement purposes.
 - The 2024 edition of ICD-10-CM E88.1 became effective on October 1, 2022.
 - This is the American ICD-10-CM version of E88.1 – other international versions of ICD-10 E88.1 may differ.
 
ICD-10-CM E88.1 is grouped within Diagnostic Related Group(s):
- 642 Inborn and other disorders of metabolism
 
Applicable To
- Lipodystrophy NOS
 
Type 1 Excludes
- Whipple’s disease (K90.81)
 
Code History
- 2016 (effective 10/1/2015): New code (first year of non-draft ICD-10-CM)
 - 2016 (effective 10/1/2015): No change
 - 2017 (effective 10/1/2016): No change
 - 2018 (effective 10/1/2017): No change
 - 2019 (effective 10/1/2018): No change
 - 2020 (effective 10/1/2019): No change
 - 2021 (effective 10/1/2020): No change
 - 2022 (effective 10/1/2021): No change
 - 2023 (effective 10/1/2022): No change
 - 2024 (effective 10/1/2023): No change
 - 2025 (effective 10/1/2024): No change
 
Diagnosis Index entries containing back-references to E88.1:
- Barraquer (-Simons\’) (progressive lipodystrophy) > Disease, diseased
 - Simons\’ (progressive lipodystrophy) > Disease, diseased
 - insulin > Lipodystrophy (progressive) E88.1
 - Hollander-Simons > Syndrome
 - Simons\’ > Syndrome
 
